Familial Q-T prolongation syndrome with Mobitz-Ⅱtype Ⅱ°A-V block

A case of familial Q-T prolongation syndrome with Mobitz-Ⅱtype Ⅱ° A-V block was reported. This syndrome is clinically characterited by recurrent faintings and sudden death in some cases. Many investigators believe that ECG changes are due to asymmetrical action of sympathefic ner- vation on the myocardium,resulting in an imbalance of repolarization process,which,in turn,leads to setious ventricular arrhythmias.This case was complicated with Mobitz-Ⅱ type Ⅱ° A-V block which was demonstrated by the intracardial His bundle recording.After admission,the patient was treated symptomatically for about one month with little effect.In general,the prognosis is ra- ther poor.