Hypertrophic interstitial neuropathy（report of 1 case）

A case of hypertrophic interstitial neuropathy（Déjérine-Sottas disease）was reported and relative literature was reviewed.The classical features of a famillial occurrence,usually symmetrical involvement,and slowly evolving polyneuropathy with palpably enlarged peripheral nerves and without pes cavus or trophic ulcers ordinarily suffives for the accurate diagnosis.Peripheral nerve biopsy may be particularly helpful.The biopsy results of nervus cutaneus surae lateralis was reported.In 1975,Dyck classified this type of disease as a hereditary motor sensory neuropathy（HMSN）,type Ⅲ.