Abstract: Objective To summarize the clinical features of congenital bicuspid aortic valve and its surgical treatment experiences. Methods Thirty-four patients with congenital bicuspid aortic valve(28 males and 6 females) at the age of 23-78 years(range 51.0±12.4 years),who underwent surgery in our department from January 2008 to December 2010,were retrospectively analyzed.Of these patients,10(29.4%) were diagnosed with pure aortic stenosis,5(14.7%) with pure aortic incompetency,19(55.8%) with aortic incompetency due to stenosis,6(17.6%) with infectious endocarditis,30(88.2%) with aortic root dilatation,32 underwent simple aortic valve replacement,1 Bentall procedure,and 1 aortic valve replacement + ascending aorta replacement.Of these patients,21 underwent mechanical valve replacement,and 12 underwent bioprosthetic valve replacement. Results No death and severe complication occurred.The ascending aortic diameter and LVEDD were smaller after operation than before operation((45.4±5.9)mm vs(40.9±6.5)mm,(56.9±15.5)mm vs(44.3±9.0)mm,P<0.05). Conclusion Congenital bicuspid aortic valve should be treated with different surgical procedures according to its condition.