薛新颖, 王娜, 薛庆亮, 张丽娜, 郭丽娜, 李新甫, 汪建新. 以多发囊肿为征象的叶内型肺隔离征1例并文献复习[J]. 解放军医学院学报, 2012, 33(1): 88-89101. DOI: CNKI:11-3275/R.20110718.1516.003
引用本文: 薛新颖, 王娜, 薛庆亮, 张丽娜, 郭丽娜, 李新甫, 汪建新. 以多发囊肿为征象的叶内型肺隔离征1例并文献复习[J]. 解放军医学院学报, 2012, 33(1): 88-89101. DOI: CNKI:11-3275/R.20110718.1516.003
XUE Xin-ying, WANG Na, XUE Qing-liang, ZHANG Li-na, GUO Li-na, LI Xin-fu, WANG Jian-xin. Intralobar pulmonary sequestration characterized by multiple cysts:A case report with literature review[J]. ACADEMIC JOURNAL OF CHINESE PLA MEDICAL SCHOOL, 2012, 33(1): 88-89101. DOI: CNKI:11-3275/R.20110718.1516.003
Citation: XUE Xin-ying, WANG Na, XUE Qing-liang, ZHANG Li-na, GUO Li-na, LI Xin-fu, WANG Jian-xin. Intralobar pulmonary sequestration characterized by multiple cysts:A case report with literature review[J]. ACADEMIC JOURNAL OF CHINESE PLA MEDICAL SCHOOL, 2012, 33(1): 88-89101. DOI: CNKI:11-3275/R.20110718.1516.003

以多发囊肿为征象的叶内型肺隔离征1例并文献复习

Intralobar pulmonary sequestration characterized by multiple cysts:A case report with literature review

  • 摘要: 目的 探讨叶内型肺隔离症(intralobar pulmonary sequestration,IPS)的临床特征、诊断和治疗。 方法 报道叶内型肺隔离症1例,并进行文献复习。 结果 患者女性,34岁,平素常有咳嗽、咳痰症状,增强CT示多发囊性密度影,无强化,周边不规则,囊腔壁可见异常受压迂曲血管影,血管来自腹腔动脉干,诊断右下肺叶内型肺隔离症。 结论 以多发囊肿为表现的叶内型肺隔离症临床上十分少见,极易误诊。增强CT+三维重建是诊断此病的首选方法,如能早期诊断、早期治疗并预防感染等并发症,预后较好。

     

    Abstract: Objective To study the clinical features,diagnosis and treatment of intralobar pulmonary sequestration(IPS). Methods One case of IPS was reported with its related literature reviewed. Results The patient was a 34-year-old female.Her main symptoms were cough and sputum.Enhanced CT showed a multiple cystic-density shadow,cyst wall-compressed abnormal vessels,but no enhancement and peripheral irregularity,thus IPS was diagnosed. Conclusion IPS with multi-cysts is a rare disease,which is easily misdiagnosed in clinical practice.Enhanced CT and 3-dimensional reconstruction are the first choice of its diagnosis.Its early diagnosis and treatment can prevent complications such as infection and can thus achieve a good prognosis.

     

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